| A Case of CHAP Syndrome |
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Man Wook Seo, Ji Sung Kim, Seong Yong Yu, Byeung Soo Shin, Young Hyun Kim |
| CHAP 증후군 1예 |
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| Abstract |
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CHAP syndorme consists of choreoathetosis, orofacial dyskinesia, affective change, hypotonia, and pseudobulbar signs. CHAP syndrome was firstly des- cribed with onset 1 to 7 days after induced profound hypothermia and complete circulatory arrest for con- genital heart lesion repair. Since then, only a few cases have been reported until now. Case We report a patient who demonstrated all of the elements of the CHAP syndrome in severe cachexic state. Brain SPECT(99mTC-ECD) shows decreased perfusion in left fronto-parieto-temporal lobe. Comments The pathogenesis of CHAP syndrome is obscure. However our case led us to suggest that more essential component pre- disposing to the CHAP syndrome is hypoxia rather than hypothermia. Furthermore, it seems to be related with circulatory insufficiency in extrapyramidal nervous systems. |
| Key Words:
Choreoathetosis, Orofacial dyskinesia, Hypotonia, Pseudobular signs |
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